ird ventricular chordoid meningioma or chordoma: a diagnostic dilemma based on a single case

We report a case and literature review of a rare third ventricular tumor in a child with histologic characteristics of chordoma and chordoid meningioma (CM). Case: A 13-year-old boy was diagnosed with a recurrent intraventricular tumor 22 months aft er complete surgical removal. Reoperation was indicated; treatment consisted of total microsurgical removal, histologic and immunohistochemical classifi cation, and follow up. Literature review on Pub Med was performed using the Mesh key words: “Cerebral Ventricle Neoplasms” AND “Pediatrics”. Histologic and immunohistochemical analysis aft er the fi rst operation had shown chordoma, and second histologic and extended immunohistochemical analysis showed positivity for D2-40 marker, which is negative in chordoma but can be positive in CM. It was concluded to be a case of CM. Fourteen months aft er reoperation there were no signs of tumor recurrence. Literature review showed two cases of intraventricular CM, one situated in lateral ventricle and the other in third ventricle. Conclusion: Th is is the second reported case of CM situated in the third ventricle in a pediatric patient. In this case, follow up was performed regularly for 22 months aft er the fi rst complete resection, when the tumor recurred. First histologic and immunohistochemical analysis showed chordoma, whereas second analysis showed CM. Fourteen months aft er reoperation there were no signs of tumor relapse. Th e boy returned to his everyday activities, with some hormone misbalance treated with hormone substitutes.